Q04.1

Billable

Arhinencephaly

Q04.1 is the ICD-10-CM code for Arhinencephaly. It is a billable, specific code valid for reimbursement.

Status
Billable
Chapter
Q00-Q99
Parent
Q04
Edition
FY2026

Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities

What this means — in plain language

MedlinePlus · NIH

Most brain malformations begin long before a baby is born. Something damages the developing nervous system or causes it to develop abnormally. Sometimes it's a genetic problem. In other cases, exposure to certain medicines , infections , or radiation during pregnancy interferes with brain development. Parts of the brain may be missing, abnormally small or large, or not fully developed. Treatment depends upon the…

Read more about Brain Malformations at MedlinePlus ↗

Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.

No additional coding notes for this code.

Frequently asked questions

What is ICD-10 code Q04.1?
Q04.1 is the ICD-10-CM code for "Arhinencephaly". It falls under Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities.
Is Q04.1 a billable code?
Yes — Q04.1 is a billable, specific ICD-10-CM code valid for reimbursement.

Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.

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