Q98.1

Billable

Klinefelter syndrome, male with more than two X chromosomes

Q98.1 is the ICD-10-CM code for Klinefelter syndrome, male with more than two X chromosomes. It is a billable, specific code valid for reimbursement.

Status
Billable
Chapter
Q00-Q99
Parent
Q98
Edition
FY2026

Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities

What this means — in plain language

MedlinePlus · NIH

What is Klinefelter syndrome (KS)? Klinefelter syndrome (KS) is a genetic condition that happens when a male is born with an extra copy of the X chromosome. KS can affect different stages of physical, language, and social development. It also usually causes infertility . What causes Klinefelter syndrome (KS)? KS is not inherited. It's caused by a random error that happens when a sperm or egg is formed. This error…

Read more about Klinefelter Syndrome at MedlinePlus ↗

Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.

No additional coding notes for this code.

Frequently asked questions

What is ICD-10 code Q98.1?
Q98.1 is the ICD-10-CM code for "Klinefelter syndrome, male with more than two X chromosomes". It falls under Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities.
Is Q98.1 a billable code?
Yes — Q98.1 is a billable, specific ICD-10-CM code valid for reimbursement.

Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.

Look up another ICD-10 code or condition

Powered by Eleplan

Free ICD-10 lookup is just the start. Eleplan keeps the whole care plan in one place.

Diagnoses, medications, documents, appointments, and the whole care team — organized and always in sync, with Ellie, your AI care assistant, on top of it. Free to start.