E76.0
Non-billableMucopolysaccharidosis, type I
E76.0 is the ICD-10-CM code for Mucopolysaccharidosis, type I. It is a non-billable category code — use a more specific child code such as E76.01 for billing.
E00-E89 Endocrine, nutritional and metabolic diseases
What this means — in plain language
MedlinePlus · NIHMucopolysaccharidosis type I (MPS I) is a condition that affects many parts of the body. This disorder was once divided into three separate syndromes: Hurler syndrome (MPS I-H), Hurler-Scheie syndrome (MPS I-H/S), and Scheie syndrome (MPS I-S), listed from most to least severe. Because there is so much overlap between each of these three syndromes, MPS I is currently divided into the severe and attenuated types.…
Read more about Mucopolysaccharidosis type I at MedlinePlus ↗Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.
Medications indicated for this condition
FDA labeling- Elosulfase AlfaHydrolytic Lysosomal Glycosaminoglycan-specific Enzyme [EPC]›
- GalsulfaseHydrolytic Lysosomal Glycosaminoglycan-specific Enzyme [EPC]›
- IdursulfaseHydrolytic Lysosomal Glycosaminoglycan-specific Enzyme [EPC]›
- LaronidaseHydrolytic Lysosomal Glycosaminoglycan-specific Enzyme [EPC]›
- Tividenofusp Alfa›
- Vestronidase AlfaLysosomal beta Glucuronidase [EPC]›
Drugs whose FDA labeling lists this condition's category among its indications. Informational only — not a treatment recommendation or medical advice.
Frequently asked questions
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
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