E88.01
BillableAlpha-1-antitrypsin deficiency
E88.01 is the ICD-10-CM code for Alpha-1-antitrypsin deficiency. It is a billable, specific code valid for reimbursement.
E00-E89 Endocrine, nutritional and metabolic diseases
What this means — in plain language
MedlinePlus · NIHWhat is alpha-1 antitrypsin deficiency (AAT deficiency)? Alpha-1 antitrypsin deficiency (AAT deficiency, or AATD) is an inherited condition that raises your risk for lung and liver disease. If you have this condition, your body doesn't make enough alpha-1 antitrypsin (AAT). AAT is made by your liver. It helps protect your lungs from inflammation and irritating substances you might breathe in, such as smoke. If your…
Read more about Alpha-1 Antitrypsin Deficiency at MedlinePlus ↗Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.
Includes
- •AAT deficiency
Frequently asked questions
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
Look up another ICD-10 code or condition