Q00

Non-billable

Anencephaly and similar malformations

Q00 is the ICD-10-CM code for Anencephaly and similar malformations. It is a non-billable category code — use a more specific child code such as Q00.0 for billing.

Status
Header (non-billable)
Chapter
Q00-Q99
Subcodes
3
Edition
FY2026

Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities

What this means — in plain language

MedlinePlus · NIH

Neural tube defects are birth defects of the brain, spine, or spinal cord. They happen in the first month of pregnancy, often before a woman even knows that she is pregnant. The two most common neural tube defects are spina bifida and anencephaly. In spina bifida, the fetal spinal column doesn't close completely. There is usually nerve damage that causes at least some paralysis of the legs. In anencephaly, most of…

Read more about Neural Tube Defects at MedlinePlus ↗

Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.

No additional coding notes for this code.

Frequently asked questions

What is ICD-10 code Q00?
Q00 is the ICD-10-CM code for "Anencephaly and similar malformations". It falls under Q00-Q99 Congenital malformations, deformations and chromosomal abnormalities.
Is Q00 a billable code?
No — Q00 is a non-billable header code. Use a more specific child code (such as Q00.0) for billing.
What are the subcodes of Q00?
Q00 has 3 more specific child codes, including Q00.0, Q00.1, Q00.2.

Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.

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