D76.1
BillableHemophagocytic lymphohistiocytosis
D76.1 is the ICD-10-CM code for Hemophagocytic lymphohistiocytosis. It is a billable, specific code valid for reimbursement.
D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism
What this means — in plain language
MedlinePlus · NIHFamilial hemophagocytic lymphohistiocytosis is a disorder in which the immune system produces too many activated immune cells (lymphocytes) called T cells, natural killer cells, B cells, and macrophages (histiocytes). Excessive amounts of immune system proteins called cytokines are also produced. This overactivation of the immune system causes fever and damages the liver and spleen, resulting in enlargement of these…
Read more about Familial hemophagocytic lymphohistiocytosis at MedlinePlus ↗Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.
Includes
- •Familial hemophagocytic reticulosis
- •Histiocytoses of mononuclear phagocytes
Medications indicated for this condition
FDA labelingDrugs whose FDA labeling lists this condition's category among its indications. Informational only — not a treatment recommendation or medical advice.
Frequently asked questions
- What is ICD-10 code D76.1?
- D76.1 is the ICD-10-CM code for "Hemophagocytic lymphohistiocytosis". It falls under D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism.
- Is D76.1 a billable code?
- Yes — D76.1 is a billable, specific ICD-10-CM code valid for reimbursement.
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
Look up another ICD-10 code or condition