E84.0
BillableCystic fibrosis with pulmonary manifestations
E84.0 is the ICD-10-CM code for Cystic fibrosis with pulmonary manifestations. It is a billable, specific code valid for reimbursement.
E00-E89 Endocrine, nutritional and metabolic diseases
What this means — in plain language
MedlinePlus · NIHCystic fibrosis (CF) is an inherited disease of the mucus and sweat glands. It affects mostly your lungs, pancreas, liver, intestines, sinuses, and sex organs. CF causes your mucus to be thick and sticky. The mucus clogs the lungs, causing breathing problems and making it easy for bacteria to grow. This can lead to repeated lung infections and lung damage. The symptoms and severity of CF can vary. Some people have…
Read more about Cystic Fibrosis at MedlinePlus ↗Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.
Use additional code
- •code to identify any infectious organism present, such as:
- •Pseudomonas (B96.5)
Medications indicated for this condition
FDA labeling- Leucovorin›
- IvacaftorCystic Fibrosis Transmembrane Conductance Regulator Potentiator [EPC]›
- TezacaftorCystic Fibrosis Transmembrane Conductance Regulator Potentiator [EPC]›
- Tobramycin SolutionAminoglycoside Antibacterial [EPC]›
Drugs whose FDA labeling lists this condition's category among its indications. Informational only — not a treatment recommendation or medical advice.
Conditions mapped to this code
MedlinePlus · NIHPlain-language health-topic references grounded in MedlinePlus (NIH/NLM).
Frequently asked questions
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
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