I27.0
BillablePrimary pulmonary hypertension
I27.0 is the ICD-10-CM code for Primary pulmonary hypertension. It is a billable, specific code valid for reimbursement.
I00-I99 Diseases of the circulatory system
What this means — in plain language
MedlinePlus · NIHWhat is pulmonary hypertension? Pulmonary hypertension, sometimes called PH, is a serious condition that affects the blood vessels in the lungs. It develops when the blood pressure in your lungs is higher than normal. Your heart pumps blood to your lungs so they can add oxygen to the blood. The blood goes back to your heart. From there, it travels to the rest of your body so that your tissues can get the oxygen that…
Read more about Pulmonary Hypertension at MedlinePlus ↗Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.
Includes
- •Heritable pulmonary arterial hypertension
- •Idiopathic pulmonary arterial hypertension
- •Primary group 1 pulmonary hypertension
- •Primary pulmonary arterial hypertension
Excludes1 — not coded here
Medications indicated for this condition
FDA labeling- SildenafilPhosphodiesterase 5 Inhibitor [EPC]›
- TreprostinilProstacycline Vasodilator [EPC]›
- MacitentanEndothelin Receptor Antagonist [EPC]›
- Nitric OxideVasodilator [EPC]›
- AmbrisentanEndothelin Receptor Antagonist [EPC]›
- Bosentan›
- EpoprostenolProstacycline Vasodilator [EPC]›
- SelexipagProstacyclin Receptor Agonist [EPC]›
- Noxivent 102Vasodilator [EPC]›
- RiociguatSoluble Guanylate Cyclase Stimulator [EPC]›
- Sildenafil Powder,›
- Sotatercept›
Drugs whose FDA labeling lists this condition's category among its indications. Informational only — not a treatment recommendation or medical advice.
Conditions mapped to this code
MedlinePlus · NIHPlain-language health-topic references grounded in MedlinePlus (NIH/NLM).
Frequently asked questions
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
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