I27.841
BillableFontan-associated lymphatic dysfunction
I27.841 is the ICD-10-CM code for Fontan-associated lymphatic dysfunction. It is a billable, specific code valid for reimbursement.
I00-I99 Diseases of the circulatory system
What this means — in plain language
MedlinePlus · NIHWhat are congenital heart defects? Congenital heart defects (CHDs) are problems with the structure of the heart. "Congenital" means that that the problems are present at birth. These defects happen when a fetus's heart doesn't develop normally during pregnancy. Congenital heart defects are the most common type of birth defect . Congenital heart defects can change the way the heart pumps blood. They may make blood…
Read more about Congenital Heart Defects at MedlinePlus ↗Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.
Notes
Medications indicated for this condition
FDA labeling- SildenafilPhosphodiesterase 5 Inhibitor [EPC]›
- TreprostinilProstacycline Vasodilator [EPC]›
- MacitentanEndothelin Receptor Antagonist [EPC]›
- Nitric OxideVasodilator [EPC]›
- AmbrisentanEndothelin Receptor Antagonist [EPC]›
- Bosentan›
- EpoprostenolProstacycline Vasodilator [EPC]›
- SelexipagProstacyclin Receptor Agonist [EPC]›
- Noxivent 102Vasodilator [EPC]›
- RiociguatSoluble Guanylate Cyclase Stimulator [EPC]›
- Sildenafil Powder,›
- Sotatercept›
Drugs whose FDA labeling lists this condition's category among its indications. Informational only — not a treatment recommendation or medical advice.
Conditions mapped to this code
MedlinePlus · NIHPlain-language health-topic references grounded in MedlinePlus (NIH/NLM).
Frequently asked questions
Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.
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