M04.2

Billable

Cryopyrin-associated periodic syndromes

M04.2 is the ICD-10-CM code for Cryopyrin-associated periodic syndromes. It is a billable, specific code valid for reimbursement.

Status
Billable
Chapter
M00-M99
Parent
M04
Edition
FY2026

M00-M99 Diseases of the musculoskeletal system and connective tissue

What this means — in plain language

MedlinePlus · NIH

Cryopyrin-associated periodic syndromes (CAPS) are a group of conditions that have overlapping signs and symptoms and the same genetic cause. The group includes three conditions known as familial cold autoinflammatory syndrome type 1 (FCAS1), Muckle-Wells syndrome (MWS), and neonatal-onset multisystem inflammatory disorder (NOMID). These conditions were once thought to be distinct disorders but are now considered to…

Read more about Cryopyrin-associated periodic syndromes at MedlinePlus ↗

Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.

Includes

  • Chronic infantile neurological, cutaneous and articular syndrome [CINCA]
  • Familial cold autoinflammatory syndrome
  • Familial cold urticaria
  • Muckle-Wells syndrome
  • Neonatal onset multisystemic inflammatory disorder [NOMID]

Frequently asked questions

What is ICD-10 code M04.2?
M04.2 is the ICD-10-CM code for "Cryopyrin-associated periodic syndromes". It falls under M00-M99 Diseases of the musculoskeletal system and connective tissue.
Is M04.2 a billable code?
Yes — M04.2 is a billable, specific ICD-10-CM code valid for reimbursement.

Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.

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