D81.818

Billable

Other biotin-dependent carboxylase deficiency

D81.818 is the ICD-10-CM code for Other biotin-dependent carboxylase deficiency. It is a billable, specific code valid for reimbursement.

Status
Billable
Chapter
D50-D89
Parent
D81.81
Edition
FY2026

D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism

What this means — in plain language

MedlinePlus · NIH

What is the immune system? Your immune system is a complex network of cells, tissues, and organs. Together they help the body fight infections and other diseases. When germs such as bacteria or viruses invade your body, they attack and multiply. This is called an infection. The infection causes the disease that makes you sick. Your immune system protects you from the disease by fighting off the germs. What are the…

Read more about Immune System and Disorders at MedlinePlus ↗

Source: U.S. National Library of Medicine (MedlinePlus). Informational only — not medical advice.

Includes

  • Holocarboxylase synthetase deficiency
  • Other multiple carboxylase deficiency

Frequently asked questions

What is ICD-10 code D81.818?
D81.818 is the ICD-10-CM code for "Other biotin-dependent carboxylase deficiency". It falls under D50-D89 Diseases of the blood and blood-forming organs and certain disorders involving the immune mechanism.
Is D81.818 a billable code?
Yes — D81.818 is a billable, specific ICD-10-CM code valid for reimbursement.

Source: CMS ICD-10-CM FY2026. For informational purposes only — not medical advice. See our medical disclaimer.

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